Short-lasting unilateral neuralgiform headache attacks: Clinical features and diagnosis
- Manjit S Matharu, MD
Manjit S Matharu, MD
- Consultant Neurologist
- The National Hospital for Neurology and Neurosurgery, London
- Anna S Cohen, MD
Anna S Cohen, MD
- Consultant Neurologist
- Royal Free Hospital, London
- Section Editor
- Jerry W Swanson, MD, MHPE
Jerry W Swanson, MD, MHPE
- Section Editor — Headache
- Professor of Neurology
- Mayo Clinic College of Medicine
INTRODUCTION AND CLASSIFICATION
The trigeminal autonomic cephalalgias (TACs) are a group of primary headache disorders characterized by unilateral trigeminal distribution pain that occurs in association with ipsilateral cranial autonomic features [1,2]. The TACs include cluster headache, paroxysmal hemicrania, short-lasting unilateral neuralgiform headache attacks, and hemicrania continua .
Despite their common elements, the TACs differ in attack duration and frequency, as well as the response to therapy (table 1).
●Hemicrania continua is characterized by continuous pain with exacerbations
●Cluster headache has a relatively long attack duration and relatively low attack frequency
●Paroxysmal hemicrania has intermediate duration and intermediate attack frequencyTo continue reading this article, you must log in with your personal, hospital, or group practice subscription. For more information on subscription options, click below on the option that best describes you:
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- INTRODUCTION AND CLASSIFICATION
- HISTORICAL ASPECTS
- CLINICAL FEATURES
- Site of pain
- Duration, frequency and temporal profile of individual attacks
- Interictal pain
- Family history
- Lack of refractory period
- Neurologic examination
- Diagnostic criteria
- Distinguishing features
- Response to treatment
- DIFFERENTIAL DIAGNOSIS
- Trigeminal neuralgia
- Secondary headache
- - Posterior fossa lesions
- - Pituitary lesions
- - Trigeminal neurovascular loop
- SUMMARY AND RECOMMENDATIONS