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Myopathies affecting the extraocular muscles in children

Andrew G Lee, MD
Paul W Brazis, MD
Section Editors
Evelyn A Paysse, MD
Marc C Patterson, MD, FRACP
Deputy Editor
Carrie Armsby, MD, MPH


Most generalized myopathies do not affect the extraocular muscles. However, there are some notable exceptions. Chronic progressive external ophthalmoplegia (CPEO) is a nonspecific term that is used to describe a range of myopathies that affect the extraocular muscles. These progressive ophthalmoplegias include:

Isolated CPEO

Kearns-Sayre syndrome

Oculopharyngeal muscular dystrophy

Myotonic dystrophy

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Literature review current through: Nov 2017. | This topic last updated: Mar 23, 2017.
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