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Clinical manifestations, pathologic features, and diagnosis of hepatosplenic T cell lymphoma

Arnold S Freedman, MD
Jon C Aster, MD
Section Editor
Andrew Lister, MD, FRCP, FRCPath, FRCR
Deputy Editor
Alan G Rosmarin, MD


The peripheral T cell lymphomas (PTCLs) are a heterogeneous group of generally aggressive neoplasms that constitute less than 15 percent of all non-Hodgkin lymphomas (NHLs) in adults. (See "Classification of the hematopoietic neoplasms".)

Among these, in decreasing frequency of occurrence, are:

Peripheral T cell lymphoma, not otherwise specified (NOS)

Anaplastic large cell lymphoma, primary systemic type

Angioimmunoblastic T cell lymphoma

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Literature review current through: Nov 2017. | This topic last updated: Oct 28, 2016.
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