Clinical manifestations, pathologic features, and diagnosis of enteropathy-associated T cell lymphoma
- Arnold S Freedman, MD
Arnold S Freedman, MD
- Section Editor — Lymphoproliferative Disorders
- Professor of Medicine
- Harvard Medical School
- Jon C Aster, MD
Jon C Aster, MD
- Professor of Pathology
- Harvard Medical School
The peripheral T cell lymphomas (PTCLs) are a heterogeneous group of generally aggressive neoplasms that constitute less than 15 percent of all non-Hodgkin lymphomas (NHLs) in adults. (See "Classification of the hematopoietic neoplasms".)
Among these, in decreasing frequency of occurrence, are [1,2]:
●Peripheral T cell lymphoma, not otherwise specified
●Anaplastic large cell lymphoma, primary systemic type
●Angioimmunoblastic T cell lymphomaTo continue reading this article, you must log in with your personal, hospital, or group practice subscription. For more information on subscription options, click below on the option that best describes you:
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- CLINICAL FEATURES
- - Tumor
- - Adjacent mucosa
- Genetic features
- DIFFERENTIAL DIAGNOSIS
- Refractory celiac disease
- Monomorphic epitheliotropic intestinal T cell lymphoma
- Indolent T cell lymphoproliferative disease
- Extranodal NK/T cell lymphoma
- Gamma-delta T cell lymphoma
- Anaplastic large cell lymphoma
- B cell lymphomas