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Clinical manifestations and diagnosis of pulmonic stenosis in adults

Karen Stout, MD
Section Editor
Heidi M Connolly, MD, FASE
Deputy Editor
Susan B Yeon, MD, JD, FACC


Stenosis of the pulmonary valve is a relatively common congenital defect, occurring in approximately 10 percent of children with congenital heart disease [1]. There is a slight female predominance, and familial occurrence has been reported in 2 percent of cases [2].

Pulmonic stenosis in children is usually associated with a benign clinical course, and excellent treatment options are available for severe cases. Thus, there is a high rate of survival into adulthood. This topic will review the pathophysiology, clinical manifestations, and diagnosis of pulmonic stenosis. The natural history and treatment of this disorder are discussed separately. (See "Natural history and treatment of pulmonic stenosis in adults".)


Pulmonic stenosis can occur at three locations:



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Literature review current through: Nov 2017. | This topic last updated: Jul 20, 2016.
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