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Classification and prognosis of pulmonary hypertension in adults

Lewis J Rubin, MD
William Hopkins, MD
Section Editor
Jess Mandel, MD
Deputy Editor
Geraldine Finlay, MD


Pulmonary hypertension (PH) is defined as an elevated mean arterial pressure ≥25 mmHg at rest [1,2]. PH has several etiologies and can be a progressive, fatal disease, if untreated.

The classification and prognosis of PH are reviewed here. The epidemiology, pathogenesis, clinical features, diagnostic evaluation, and treatment of PH are discussed separately. (See "The epidemiology and pathogenesis of pulmonary arterial hypertension (Group 1)" and "Clinical features and diagnosis of pulmonary hypertension in adults" and "Treatment of pulmonary hypertension in adults".)


The World Health Organization (WHO) has classified PH based upon etiology into the five groups listed below (table 1) [1,2]:

Group 1 – Pulmonary arterial hypertension (PAH)

Group 2 – PH due to left heart disease

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Literature review current through: Nov 2017. | This topic last updated: Oct 27, 2017.
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