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Appendiceal mucoceles

Louis-Michel Wong Kee Song, MD, FRCP(C)
Norman E Marcon, MD, FRCP(C)
Section Editor
J Thomas Lamont, MD
Deputy Editor
Wenliang Chen, MD, PhD


Appendiceal mucoceles are rare and are characterized by a distended, mucus-filled appendix. The course and prognosis of appendiceal mucoceles relate to their histologic subtypes.

This topic will review the epidemiology, clinical manifestations, diagnosis, and management of appendiceal mucoceles. Other causes of ileocecal lesions, including tuberculosis, typhlitis, actinomycosis, carcinoid, and lesions due to nonsteroidal anti-inflammatory drugs (NSAIDs), are discussed separately. (See "Neutropenic enterocolitis (typhlitis)" and "Abdominal actinomycosis" and "Clinical characteristics of carcinoid tumors" and "NSAIDs: Adverse effects on the distal small bowel and colon" and "Abdominal tuberculosis".)


An appendiceal mucocele refers to any lesion that is characterized by a distended, mucus-filled appendix. Mucoceles may be due to non-neoplastic or neoplastic lesions.

Appendiceal mucoceles can be classified into the following histologic subtypes:

Mucosal hyperplasia is histologically similar to a hyperplastic colon polyp.

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Literature review current through: Nov 2017. | This topic last updated: Sep 18, 2017.
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