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肾上腺皮质肿瘤的临床表现及评估

Author
André Lacroix, MD
Section Editor
Lynnette K Nieman, MD
Deputy Editor
Kathryn A Martin, MD
Translators
张进安, 主任医师，教授

引言

单侧肾上腺的肿瘤或包块很常见。可分为功能性(激素分泌性)或无症状性，以及良性或恶性。

●大多数肾上腺皮质肿瘤是在腹部影像学检查中被偶然发现的良性无功能性腺瘤(肾上腺偶发瘤)。 (参见“肾上腺偶发瘤”)

●其他肾上腺皮质肿瘤则为良性激素分泌性腺瘤，可引起库欣综合征、原发性醛固酮增多症，或是远远更少见的男性化表现。

●肾上腺皮质癌(adrenocortical carcinoma, ACC)较罕见，通常为侵袭性肿瘤，可能为功能性肿瘤并引起库欣综合征和/或男性化，或为无功能性肿瘤并表现为腹部肿块或偶然发现。

●嗜铬细胞瘤是起源自肾上腺髓质嗜铬细胞的儿茶酚胺分泌型肿瘤，可为良性或恶性。相关内容将单独讨论。 (参见“成人嗜铬细胞瘤的治疗”)

                           

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Literature review current through: 2017-06 . | This topic last updated: 2017-03-27.
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