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Vascular rings

INTRODUCTION

Vascular rings are congenital anomalies of the aortic arch that result in compression of the tracheobronchial tree and/or esophagus, leading to respiratory and gastrointestinal symptoms. They can be classified as either complete, when both the trachea and esophagus are fully encircled by a vascular anomaly, or incomplete without full encirclement of both structures.

The different forms of vascular rings and slings, and their clinical manifestations, diagnosis, and treatment are discussed here.

ANATOMY

Beginning at the fourth week of embryogenesis, the aortic arch develops from six symmetrical paired aortic arch vessels and the paired dorsal aortae. During the next few weeks of embryogenesis, remodeling and rearrangement of these structures result in the formation of the normal left aortic arch [1].

The right and left third arches persist as the right and left carotid arteries

The left fourth arch persists as the transverse arch

                      

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Literature review current through: Sep 2014. | This topic last updated: Sep 19, 2014.
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References
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