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Tricuspid valve (TV) atresia

Sowmya Balasubramanian, MD, MSc
Theresa Tacy, MD
Section Editor
John K Triedman, MD
Deputy Editor
Carrie Armsby, MD, MPH


Tricuspid valve (TV) atresia is a cyanotic congenital heart lesion that is characterized by congenital agenesis or absence of the tricuspid valve, resulting in no direct communication between the right atrium and ventricle [1]. If untreated, TV atresia has a high mortality rate with a survival rate as low as 10 percent at one year of age, depending on the type of TV atresia and the presence of other cardiac lesions [2,3].

The constellation of anatomic variants, physiology, clinical presentation, diagnosis, and management of TV atresia will be reviewed here.


TV atresia is the third most common cyanotic heart lesion with an estimated prevalence of 0.5 to 1.2 per 10,000 live births [4-7]. There is no difference in the incidence based on gender.


Although TV atresia is characterized by the absence of the TV, there is a spectrum of anatomic variants based on the morphology of the atresia and the presence of other cardiac structural lesions.

Morphology of TV atresia — Morphologic variation of TV atresia includes the following [8,9]:

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Literature review current through: Nov 2017. | This topic last updated: Feb 24, 2016.
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