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Treatment of relapsing polychondritis

INTRODUCTION

It is difficult to predict the clinical course of relapsing polychondritis (RPC) because there is a marked inter-patient variability (see "Clinical manifestations of relapsing polychondritis") The patterns that may be seen include:

Episodic disease activity.

Smoldering disease with ever-changing severity.

A fulminant downhill course resulting in death.

A relatively benign course that is free of clinically evident visceral involvement and is easily managed. It is not possible to estimate the prevalence of this self-limited pattern, since it is likely that many of these cases are not diagnosed.

                          

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Literature review current through: Mar 2014. | This topic last updated: Nov 7, 2013.
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