INTRODUCTION — Medical therapy is central to the management of inflammatory bowel disease (IBD). (See "Overview of the medical management of mild to moderate Crohn's disease in adults" and "Medical management of ulcerative colitis".) However, appropriate surgical treatment is an important part of therapy since it can alleviate symptoms, address serious complications, improve quality of life, and, in some settings, be lifesaving [1]. As many as one-half of patients with IBD require at least one surgical procedure during the course of their disease, however, due to earlier diagnosis and medical management, the need for surgical intervention within the first two years of diagnosis has decreased [2].
The need for and timing of an operation are best determined by interaction among the gastroenterologist, surgeon, and patient. Guidelines for the surgical treatment of ulcerative colitis have been proposed by the American Society of Colon and Rectal Surgeons [3].
PREOPERATIVE CARE — The best results from surgery occur in patients who have been well prepared medically and psychologically, who undergo the surgery in a timely and expert fashion, and who receive careful postoperative care. Although the majority of patients with IBD are young, they are often seriously ill when surgery is contemplated. Complications are more likely in patients who are malnourished, immunosuppressed, depressed, or have infection. Thus, these features must be anticipated and recognized. The adequacy of nonsurgical therapy, the extent of IBD, and previous operative and pathology reports must be reviewed.
Optimization of medical status — The patient's medical status should be optimized. Correction of anemia, fluid depletion, electrolyte and acid-base disorders, and nutritional assessment are mandatory. Many patients require total parenteral nutrition (TPN) and bowel rest because eating may worsen symptoms. However, long intervals of preoperative TPN are rarely justified, because it is difficult to demonstrate a significant impact on the ultimate outcome [4]. The simplest surgical corrective procedure should be performed in such severely compromised patients. (See "Nutritional issues in the surgical patient".)
Specific complications related to medications or coexisting diseases should be sought (table 1). Disability from medications such as cyclosporine is a source of concern for most surgeons. Coagulopathy due to malnutrition or malabsorption should be corrected. The severity of liver disease should be assessed in patients with sclerosing cholangitis to assess surgical risk and optimize perioperative care. (See "Assessing surgical risk in patients with liver disease".) Complications of specific medications are discussed in detail elsewhere. (See "Overview of the medical management of mild to moderate Crohn's disease in adults".)
Immunosuppressive therapy — Most immunosuppressive drugs can be discontinued just before surgery without sequelae, with the exception of corticosteroids, which must be tapered after surgery. (See "Glucocorticoid withdrawal".) Continuation of immunosuppressive therapy may also be desirable in some patients with Crohn's disease to prevent postoperative recurrence. (See "Immunomodulator therapy in Crohn's disease".)
Postoperative complications do not appear to be increased in patients with Crohn's disease treated with infliximab [5-8], although in one study the use of infliximab during the first three postoperative months after ileocolonic resection was associated with increased risk of sepsis, intra-abdominal abscess, and readmission [9]. The effects of infliximab combined with other immunomodulators are also not well studied. One study found that patients with ulcerative colitis who received infliximab and cyclosporin before colectomy had increased morbidity compared with those who received infliximab alone [10]. A multivariate analysis found infliximab to be the only factor independently associated with infectious complications in patients undergoing IPAA for chronic ulcerative colitis [11]. Preoperative use of infliximab may delay a potentially curative surgical procedure and increase the risk of serious postoperative complications. Therefore, a three-stage ileal pouch-anal canal anastomosis (IPAA) is the optimal approach for patients on combination immunosuppressive therapy that includes infliximab and requires surgical intervention.
Prospective controlled trials with high quality data are needed to support the safety of immunosuppressive therapy in the perioperative period.
Patient education — An honest, straightforward discussion of the risks and benefits of the proposed operation with the patient and family is mandatory to avoid the frustrations of unrealistic expectations. (See "Patient information: Ulcerative colitis (Beyond the Basics)".)
The patient should understand the indications for surgery, the remaining medical options, the surgical alternatives (see below), the expected outcome, including the risk of recurrence, and the potential for immediate and long-term complications of surgery. In patients who will receive an ostomy, a consultation with a stomal therapist is useful for selecting the ostomy site and reducing anxiety. (See "Management of patients with a colostomy or ileostomy".)
Prevention of infection — Adequate antibiotic prophylaxis or antibiotic therapy should be given. The mechanical bowel preparation has to be adapted to the patient's condition; as an example, it is contraindicated in patients with an acute abdomen or obstruction.
Prophylaxis for venous thrombosis — Patients with IBD are at increased risk for thromboembolic venous and arterial complications [12,13]. Thus, intermittent pneumatic compression and/or low dose heparin should be used prophylactically. (See "Prevention of venous thromboembolic disease in surgical patients".)
DISTINGUISHING BETWEEN CROHN'S DISEASE AND ULCERATIVE COLITIS — Surgical decisions and expected outcomes are influenced by the distinction between the ulcerative colitis and Crohn's disease [14,15].
Ulcerative colitis and Crohn's colitis can usually be distinguished based upon clinical presentation, radiography, endoscopy (eg, continuous colitis in ulcerative colitis compared to patchy involvement in Crohn's disease), and biopsy [14,15]. (See "Clinical manifestations, diagnosis, and prognosis of ulcerative colitis in adults" and "Clinical manifestations, diagnosis and prognosis of Crohn's disease in adults".) However, the colitis is indeterminate in 8 to 20 percent of patients; the distinction may be particularly difficult in patients with fulminant colitis [18]. The course of these patients tends to resemble that of patients with ulcerative colitis more than it does Crohn's disease, although there may be an increased risk of perineal complications and pouch failure [19,20]. Thus, many surgeons consider patients with indeterminate colitis to be candidates for the same surgical options as those with ulcerative colitis [1,21], although some prefer ileoproctostomy [22]. In a proportion of patients with colitis who do not require surgery, it can also be difficult to distinguish between ulcerative colitis and Crohn’s disease. The term inflammatory bowel disease unclassified is proposed for these cases. Further evaluation may reveal the exact type of disease in these patients [23].
INDICATIONS FOR SURGERY — Advances in medical therapy (including use of infliximab) have reduced the need for emergency surgery due to catastrophic complications such as massive hemorrhage, perforation, fulminant colitis, and acute colonic obstruction [24]. (See "Infliximab in Crohn's disease" and "Toxic megacolon".) On the other hand, the development of continence-preserving procedures such as the ileal pouch anal-canal anastomosis has made surgery a more attractive option in patients in whom medical therapy has been unsuccessful or undesirable. The treatment of choice for acute severe steroid refractory ulcerative colitis is controversial [25]. Gastroenterologists advocate a trial of infliximab [26], while surgeons favor colectomy [27]. A longer duration of in-hospital ineffective medical therapy (8 versus 5 days) that delays surgical therapy in patients with acute severe ulcerative colitis is associated with an increased risk of postoperative complications [28].
The most common indication for elective surgery is disease activity that has been intractable to medical therapy. However, "intractable" is often hard to define. Some authorities have suggested that disease should be considered intractable when it or its treatment is associated with severe and persistent impairment in the quality of life [1,29]. However, these parameters are difficult to measure and are variable among individual patients. We recommend that surgery should be considered for the following indications:
The threshold for performing surgery may be lowered by a number of other factors such as the presence of anemia or hypoproteinemia, and growth retardation in children. On the other hand, the threshold may be increased in patients with severe comorbid illnesses, or those in whom prior intestinal resection place them at risk for the development of the short bowel syndrome. (See "Pathophysiology of the short bowel syndrome".)
Extraintestinal manifestations — The relationship between extracolonic manifestations of IBD and surgery is not well defined. Extraintestinal complications alone seldom require operation but often contribute to the decision to operate. However, healing of pyoderma gangrenosum after intestinal resection is uncertain, ankylosing spondylitis and arthritis may not regress after surgery, and progression of sclerosing cholangitis appears to bear no relation to the presence or absence of the inflammatory process in the colon. A rare extracolonic indication for colectomy and splenectomy is massive hemolytic anemia that is unresponsive to medical treatment [1,30]. Thromboembolic complications that are life threatening, erythema nodosum, and arthralgia of the small and large joints appear to benefit the most from proctocolectomy [31]. Colorectal cancer is an uncommon but important complication in patients who have undergone liver transplantation for primary sclerosing cholangitis. Such patients require ongoing surveillance. (See "Colorectal cancer and primary sclerosing cholangitis".)
SURGICAL OPTIONS FOR ULCERATIVE COLITIS — There are five surgical procedures performed in single or multiple stages that can be offered to patients with ulcerative colitis who are referred for elective colectomy (table 2 and figure 1):
Each technique can improve the quality of life and reduce the risk of colonic malignancy, and each has its advantages [32,33]. Optimal results depend upon surgical expertise, the clinical setting, and careful patient selection. The patient's age, previous intestinal or anal surgery, obesity, patient occupation, liver disease, and cancer risk should all be considered. A number of specific surgical issues remain controversial, particularly the merits of avoiding a loop diverting ileostomy [34,35] and the safety and efficacy of laparoscopic approaches [36-39]. One study showed that, compared with the open procedures, laparoscopic assisted restorative proctocolectomy had a long-lasting positive impact on body image and cosmesis, particularly for women [40]. In patients with coexisting primary sclerosing cholangitis, complications from surgical management appear mostly to be related to the severity of the liver disease [41].
In emergency situations (such as toxic megacolon), abdominal colectomy with ileostomy and closure of the rectum or mucous fistula is the procedure of choice. Leaving the rectum in place permits subsequent proctectomy with ileal pouch-anal anastomosis. (See "Toxic megacolon".) Emergency proctocolectomy may also be required for uncontrollable hemorrhage. However, per anal suturing of a bleeding rectal ulcer or leaving a short Hartmann pouch can also be considered in this setting [42]. IPAA should not be performed on patients with toxic colitis due to excessively high complication rates. In addition, patients who are on combination immunosuppressive therapy that includes Infliximab may benefit from a three-stage IPAA [11].
Proctocolectomy with permanent ileostomy is curative for ulcerative colitis. However, patients with IBD wish to avoid a permanent ileostomy. Patients should be advised that an ileostomy may be required if a continence preserving procedure fails or is not technically possible. Furthermore, continence performing procedures are associated with a small risk of urinary and sexual dysfunction; the risk is greatest in patients who require reoperative pelvic surgery. Postoperative impotence and retrograde ejaculation are observed in approximately 1.5 and 4 percent of men, respectively, while transient dyspareunia occurs in about 7 percent of women. Decreased fertility is also frequent in women after IPAA. The surgeon is occasionally faced with the need to abandon the ileal pouch-anal canal anastomosis intraoperatively because of technical reasons or evidence of Crohn's disease or cancer [43,44]. In a review of almost 1800 IPAA attempts from the Mayo Clinic, abandonment was required in 4.1 percent of cases [43].
The stapled ileal pouch-distal rectal anastomosis is technically easier to perform than the ileal pouch-anal canal anastomosis and, in theory, preservation of the anal transitional mucosa should maintain anal sensation and better continence, especially at night. However, this operation leaves diseased anal and distal rectal mucosa behind. Preservation of the distal rectal mucosa should clearly be avoided in patients with cancer or severe dysplasia in the colorectal mucosa and in those with severe extraintestinal manifestations. On the other hand, it should be strongly considered in older patients, and in those in whom mobilization of the pouch to perform a tension-free anastomosis is difficult.
At our institution, an ileorectal anastomosis (IRA) has been used in fewer than 10 percent of patients undergoing surgery for ulcerative colitis, even in the era when ileal pouch-anal anastomosis (IPAA) was not available, because the IRA procedure does not excise the diseased section and thus leaves patients at risk for persistence of symptoms and future malignancy. A retrospective analysis of the functional results after IRA for ulcerative colitis or indeterminant colitis in 86 patients found that the rectum was eventually resected in 46 patients diagnosed with rectal dysplasia (17 percent), rectal cancer (8 percent), and refractory proctitis (28 percent) [45]. The cumulative probability of developing rectal dysplasia at 5, 10, 15, and 20 years was 7, 9, 20, and 25 percent, respectively. The cumulative probability of developing rectal cancer at 5, 10, 15, and 20 years was 0, 2, 5, and 14 percent, respectively. The cumulative probability of having a functioning IRA at 10 and 20 years was 74 and 46 percent, respectively.
Some patients with minimal rectal involvement may be suitable candidates such as those who are not suitable for IPAA but who refuse an ileostomy or those who have medical conditions in which a stoma is relatively contraindicate (eg, portal hypertension or ascites). Some authors have advocated the operation in women of childbearing age because of the risk of infertility. The operation may also be a good choice for patients in whom Crohn's disease cannot be excluded or for patients with colitis complicated by advanced colonic malignancy.
Satisfactory rectal function varies greatly depending upon the selections of patients and length of follow-up. The risk of cancer in the residual rectum has been reported to be 6 percent at 20 years and 15 percent at 30 years. The risk is significant considering that most patients are young and have many years to live.
Complications — Several complications and ileal pouch disorders have been recognized (table 3) [46]. Early complications are common after restorative proctocolectomy. The most frequent are bowel obstruction, pouch bleeding, pelvic and wound sepsis, transient urinary dysfunction, and dehydration from temporary loop ileostomy with high output. Most of these complications can be addressed without the need for reoperation or long-term sequelae. Exceptions are patients who develop a pelvic abscess after surgery who are at increased risk for a poor functional outcome and quality of life, and eventual pouch failure [47,48]. This was illustrated in a series from the Mayo Clinic in which 73 of 1508 (5 percent) patients who underwent ileal pouch-anal anastomosis for chronic ulcerative colitis developed a pelvic abscess [47]. The long-term impact of pelvic abscess was illustrated by the following observations:
Portal vein thrombosis can occur after IPAA. Clinical manifestations may include pain, fever, vomiting, leukocytosis, and unexplained postoperative ileus [49]. Some patients have a subtle clinical presentation and can go undiagnosed until the thrombosis is seen incidentally on computed tomography. Treatment with anticoagulation has been associated with complete recovery.
Late complications include stricture of the anastomosis, anal fistula and abscess, poor postoperative anorectal function, reduced fertility [50,51], and pouchitis [52]; of these, pouchitis is the most frequent. In one series, the cumulative probability of suffering at least one episode of clinical pouchitis was 18 and 48 percent at 1 and 10 years, respectively [52]. (See "Pouchitis".) Several other pouch disorders have been recognized such as irritable pouch syndrome and anismus (anorectal dysfunction) (figure 2) [46].
Fortunately, the majority of pouch-related complications can be addressed without surgical intervention. In one series of almost 1000 patients who had undergone IPAA, reoperation for complications was necessary in only 12 percent [53]. Local measures often suffice, but pouch revision or excision is occasionally required [53-55]. As an example, ileal pouch fistulas and strictures refractory to dilatation are difficult to treat and may require revision of the pouch if Crohn's disease can be excluded. A transvaginal repair is favored for a pouch-vaginal fistula [56]. A combined abdominal perineal repair may offer better results compared with a local procedure [57].
A controlled septic condition does not preclude salvage surgery. Although pouch failure occurs more often than with primary IPAA, high patient satisfaction and quality of life can be achieved [58]. Furthermore, excision of the pouch is associated with a high risk of complications, especially delayed perineal wound healing [59,60].
A number of unusual late complications have been described including [61-63]:
Long-term results — As discussed in the preceding section, the long-term success of surgery depends upon the type of operation, the clinical setting, and surgical expertise. Several studies have suggested that functional results are poor during the long-term follow-up in patients who had adverse personality factors before surgery (such as problems with sexual satisfaction, difficulty expressing emotions, perfectionistic body ideals, and poor frustration tolerance) [64]. The following results were described in some of the largest series:
IPAA may have long-term effects on female reproductive health [69]. Some women experience increased dyspareunia [70], although the ability to experience orgasm and coital frequency remain unchanged. Female fertility is significantly decreased [71], possibly due to pelvic adhesions, although successful pregnancies occur regularly [72]. Patients may experience a transient increase in stool frequency (including incontinence) during pregnancy, which resolves after delivery.
Pregnancy and delivery are safe in patients with IPAA. Patients should not be discouraged from childbearing because of the pouch. Whether vaginal or Cesarean delivery is better for women with a pelvic pouch remains controversial. The type of delivery should be influenced by obstetric consideration [73] but also the potential risk of sphincter injury [74]. Cesarean sections have been favored at some institutions.
Satisfactory long-term functional outcome and excellent quality of life have also been described after stapled restorative proctocolectomy. In a series of 977 patients, quality of life increased for two years after surgery, with no deterioration thereafter [75]. The prevalence of perfect continence increased from 76 percent before surgery to 82 percent after surgery and, although continence deteriorated somewhat more than two years after surgery, it was no worse than preoperative values. Ninety-eight percent of patients would have recommended the surgery to others. In another prospective, observational study, patients who had a stapled anastomosis had higher rates of daytime, nighttime, and complete continence compared with patients who underwent a hand-sewn anastomosis [76].
Postoperative monitoring — All patients who undergo surgical procedures for ulcerative colitis should be monitored regularly for the development of long-term complications [77]. In addition to functional problems, complications can occur at any stage, including the development of dysplasia and possibly cancer [78-84]. However, in a study of potentially high-risk patients (eg, Kock pouch for ≥14 years, a pelvic pouch for ≥12 years, a history of dysplasia or cancer in the proctocolectomy specimen or troublesome pouchitis), the development of dysplasia was rare [81]. These results are reassuring for both patients and surgeons [82].
Dysplasia — The presence of inflammatory changes in a retained rectal cuff, anal transitional zone, and ileal reservoir after stapled pouch-anal anastomosis is a cause of concern because of the long-term risk of dysplasia [83,85,86]. A systematic review of 23 observational and case control studies estimated that the prevalence of confirmed dysplasia in the pouch, anal transitional zone, or rectal cuff was 1.13 percent (range 0 to 19 percent) [83]. The prevalence of high-grade, low-grade, or indefinite dysplasia was 0.15, 0.98, and 1.23 percent, respectively. Dysplasia was equally frequent in the pouch and rectal cuff or anal transitional zone. Dysplasia and cancer identified before or at operation were significant predictors of the development of dysplasia postoperatively [87].
In fact, the risk of neoplasia is not completely eliminated by colectomy and mucosectomy. A retrospective review of 3203 patients with a preoperative diagnosis of IBD who underwent restorative proctocolectomy found that the cumulative incidence for pouch neoplasia at 5, 10, 15, 20 and 25 years were 0.9, 1.3, 1.9, 4.2, and 5.1 percent, respectively [87]. Eleven patients developed adenocarcinoma of the pouch or at the anal transitional zone, one developed lymphoma in the pouch, three developed squamous cell carcinoma at the anal transitional zone, and 23 developed pouch dysplasia. The prognosis of pouch adenocarcinoma appeared to be poor.
If the rectal cuff becomes symptomatic or develops dysplasia, the retained rectal mucosa from the restorative proctocolectomy can be removed by a transanal completion mucosectomy and reconstructing the ileal pouch-anal anastomosis as an alternative to a complete anal rectal resection and permanent ileostomy [88]. The mucosectomy removes all rectal mucosa, confers a highest likelihood of a surgical cure, and reduces the risk of future dysplasia. However, a mucosectomy removes the highly innervated region of cuboidal epithelium within the anal canal, with possible damage to the anal sphincter complex. Short term results in a series of 27 patients included reduced pouchitis symptoms and 90 percent of patients were moderately to very satisfied with the procedure. Incontinence was reduced by 70 percent at 12 months of observation.
These data support surveillance in patients with retained colonic mucosa. However, the optimal frequency of pouch endoscopy and biopsy is not well established. One authority recommends performing an initial screening five years after creation of an ileal pouch in children or when the total disease duration exceeds seven years [79]. It is reasonable to increase the frequency of surveillance in patients with chronic pouchitis who have severe villous atrophy and in patients who had dysplasia in the resected colon or rectum. Resection of the ileal pouch and anal canal should be considered in patients with pouch or anal high-grade dysplasia detected during surveillance.
Unrecognized Crohn's disease — A consideration in patients with pouch inflammation is whether they have unrecognized Crohn's disease. Establishing the diagnosis in patients who have undergone an IPAA can be difficult. The presence of inflammatory disease affecting other parts of the gastrointestinal tract can provide an important clue, but is not always present. One study suggested that the presence of afferent limb ulcers (in patients not taking nonsteroidal antiinflammatory drugs) was suggestive of Crohn's disease [89].
Crohn's disease involving the ileal pouch is generally associated with a high failure rate and pouch-related fistulas [17]. The complications associated with failure are extensive and the options for reconstructive surgery in patients with Crohn's disease should be questioned [90]. On the other hand, in a series of 204 patients with Crohn's disease who underwent primary IPAA overall 10 year pouch retention was 71 percent [91]. Pouch retention rates were higher and functional results were most favorable when the diagnosis of Crohn's disease was established preoperatively or immediately following surgery (85 to 87 percent 10 year pouch retention). Outcomes in patients with delayed diagnosis were worse, but half still retain their pouch at 10 years.
A systematic clinical approach to the "diseases" of the ileal pouch anal anastomosis is useful in the management of inflammatory and non-inflammatory conditions that can develop after surgery (eg, pouchitis, Crohn's disease, cuffitis, and irritable bowel syndrome) [92].
SURGICAL OPTIONS FOR CROHN'S DISEASE — Crohn's disease can potentially involve the entire gastrointestinal tract and is a chronic, diffuse, recurring disease that is not curable by surgery. As a result, surgery is usually reserved for patients in whom a complication develops or who have symptoms refractory to medical therapy [93]. The major indications for surgery are obstruction and perforation in small intestinal Crohn's disease, and chronic disability and failure to respond to medical therapy in those with colonic involvement. However, in some settings, surgery may be the most efficient means to restore health and improve quality of life, particularly in patients with short-segment stricturing or fistulizing disease [94,95]. The quality of life in patients medically treated for short segment distal ileal disease needs to be compared to surgical resection. The effectiveness of infliximab in preventing the need for surgery for Crohn’s disease at the population level has been questioned [96].
The surgical approach should focus on symptomatic areas of involvement causing complications, such as obstruction, bleeding, or perforation. Resection is performed when segments of bowel are actively or subacutely inflamed or perforated, or when there is an abscess or fistula to an adjacent organ. The disease-free margins are established by gross inspection. The presence of a few aphthous ulcers does not mandate further resection, and extensive resection margins are not necessary since microscopic disease at the margins is not associated with an increased rate of recurrence [97]. On occasion, intraoperative enteroscopy provides useful information for surgical decision making [98].
Some surgeons recommend creating a side-to-side anastomosis after ileocolonic resection because its large width may impede the development of symptomatic recurrence. However, other studies have failed to confirm this benefit [99]. A meta-analysis of eight comparative studies found that a side-to-side anastomosis was associated with fewer anastomotic leaks and postoperative complications, a shorter hospital stay and a lower perianastomotic recurrence rates compared to end-to-end anastomosis [100]. However, the authors suggested that further randomized controlled trials were needed to confirm these associations.
Laparoscopic approaches have been used increasingly for well-selected patients, even in those with recurrent disease [101-105]. They have the potential of decreasing morbidity, speeding recovery, and reducing costs, while decreasing the incidence of small bowel obstruction and ventral (abdominal wall) hernias [105-107]. A randomized controlled trial from a single institution compared laparoscopic-assisted versus open ileocolonic resection in 60 patients with Crohn's disease [108]. Morbidity, hospital stay, and costs were lower in the laparoscopic group, although there were no significant differences in quality-of-life at three months follow-up. The surgeons involved in this study were considered expert laparoscopists.
Optimal selection of patients and outcomes of laparoscopic approaches continue to be studied. One report found that the need for conversion to an open procedure was predicted by the severity of disease; independent predictors of conversion included a history of recurrent medical episodes of Crohn's disease and the presence of intra-abdominal abscess or fistula at the time of laparoscopy [109]. In a long-term follow-up study, the recurrence rates in laparoscopic ileocolic resection compared favorably with conventional surgery [110]. A policy of starting most suitable cases laparoscopically may offer patients the potential benefit of a laparoscopic approach without increased morbidity [111]. For selected patients with Crohn’s colitis, laparoscopic colectomy was found to be safe and effective in the hands of experienced surgeons [112].
Duodenal disease — Duodenal Crohn's disease seldom requires surgery. The major indications for surgery are obstruction and less often perforation or fistula formation. Gastrojejunostomy rather than resection is typically performed. Strictureplasty, duodenojejunostomy, and endoscopic balloon dilation have also been described [113].
Intra-abdominal abscess and perforation — The conventional approach to intra-abdominal pyogenic complications has been initial surgical drainage followed by resection of the diseased segment of bowel. However, the introduction of interventional procedures, new immunosuppressive agents, and laparoscopy has altered the surgical approach [114,115]. CT or ultrasound guided percutaneous drainage is safe and successful in approximately 70 percent of patients. The benefits of preoperative drainage include time to improve the patient’s nutritional status, convert the operative field into a noninfected area, and decrease use of steroids. An established abscess should preferentially be drained nonoperatively using a percutaneous approach if possible [116]. A transgluteal or transabdominal percutaneous approach to drainage can be performed depending on the location of the abscess. The procedure may need to be repeated to completely drain the abscess.
If percutaneous drainage is unsuccessful, surgical drainage should be performed. The timing of surgery following percutaneous abscess drainage, when clinically indicated, occurs after clinical resolution of sepsis. Controversy exists regarding the need for subsequent operation after adequate abscess drainage as intractable disease or recurrent abscess occurs in at least 30 percent of these patients within a year. (See 'Recurrence' below.)
Fortunately, free perforation occurs rarely in Crohn's disease. Emergent surgery is necessary to control sepsis in the presence of peritonitis. Exploratory laparotomy with construction of a stoma is most commonly required. The decision to resect bowel depends upon the operative findings and the patient's condition [116].
Abdominal wall abscesses (psoas and rectus sheath) are less common and more difficult to control locally than intra-abdominal abscesses. In a retrospective review of 13 patients with an abdominal wall abscess treated by percutaneous and/or open operative drainage, all 13 required resection of the diseased segment even after successful drainage of the abscess [115].
Fistulas — After resection and anastomosis of the diseased segment, fistulas to adjacent organs (such as the stomach, duodenum, bladder, vagina, and sigmoid colon) can be closed by suturing the site of entrance. Resection of the adjacent segment is necessary only when it is primarily involved with Crohn's disease. Bypasses should be avoided because persistent disease in the bypassed segment can lead to abscess formation, bleeding, perforation, bacterial overgrowth, and malignancy. Optimal management of perianal fistulas depends upon their anatomy. (See "Perianal complications of Crohn's disease".)
Interestingly, in one report, infliximab did not eliminate the need for surgery in the majority of patients with fistulizing Crohn's disease [117]. However, it appeared to be more effective in patients with perianal disease compared with abdominal enterocutaneous disease.
Strictures — Intestinal strictures can be relieved by resection; synchronous small bowel resection in patients with multiple strictures is common [118]. Strictureplasty or balloon dilation may be a suitable alternative for selected patients.
Strictureplasty — Strictureplasty can relieve obstruction, and is often performed with synchronous small bowel resection [118,119]. It can also be performed without excision of bowel [120,121]. Strictureplasty involves creation of a longitudinal incision through the narrowed area while closing transversely, which widens the lumen. Strictureplasty is particularly well-suited for patients who have short, localized areas of chronic stenosis, and who are at increased risk for short bowel syndrome due to previous intestinal resection [120]. It should not be performed in acutely inflamed bowel. For extensive and/or strictures occurring sequentially over long intestinal segments, a side-to-side isoperistaltic or other type of nonconventional strictureplasty is safe and effective [122-125].
Strictureplasty has been associated with excellent results, including relief of obstruction, the ability to withdraw steroids, and improvement in symptoms [120,121,126,127]. The risk of fistula or recurrent stricture formation is low and comparable to resection. Whether preservation of diseased bowel increases the long-term risk of malignancy is unknown, although case reports have documented adenocarcinoma arising from sites of previous strictureplasty [128].
The following examples illustrate the range of findings in two of the largest series [129,130]. In a report that included a total of 314 patients who underwent 1124 strictureplasty procedures [129]:
Another study included 479 strictureplasty performed in 100 patients over a period of 25 years (1978 to 2003), who were followed for an average of 7 years [130]. Overall morbidity was 22 percent (sepsis 11 percent, obstruction 4 percent, and hemorrhage 4 percent) and procedure-related mortality was 3 percent. The reoperation rates were 52 percent at a mean of 40 months after a first strictureplasty, 56 percent at 26 months after a second, 86 percent at 27 months after a third, and 63 percent at 26 months after a fourth. The major risk factor for reoperation was young age. The early relaparotomy rate was 8 percent. One patient developed cancer after many years of disease. The authors biopsied suspicious lesions, rather than routinely biopsying all lesions.
Balloon dilation — Another method to dilate intestinal strictures is with a hydrostatic balloon [131]. Experience is relatively limited compared with strictureplasty or resection, and the long-term efficacy and safety is therefore less well-established. A meta-analysis of 13 studies (with a total of 347 patients) reported overall technical success in 86 percent of cases and long-term efficacy in 58 percent, with up to 33 months of follow-up [132]. On multivariate analysis, a stricture length of ≤4 cm was associated with better surgery-free outcomes. The outcome of balloon dilatation to relieve obstruction from intestinal strictures in Crohn’s disease is not influenced by the type of concomitant medical therapy [133].
An illustrative report included 55 patients with 59 ileocolonic strictures who underwent 78 dilation procedures [134]. The procedures were performed endoscopically with patients under general anesthesia. Seventy procedures (90 percent) were technically successful. Perforation occurred in six patients (11 percent), two of whom required surgery and four of whom recovered with medical treatment. Obstructive symptoms were relieved in 62 percent of patients up to 11 months after the procedure.
Stricture injection with steroids after balloon dilatation to reduce the need for redilation or surgery may be an effective strategy for children [135] but may not be effective for adults [136]. A randomized trial that included 29 pediatric patients undergoing balloon dilatation for strictures from Crohn’s disease found significantly fewer redilations in the patients treated with corticosteroid injections compared to those who received a placebo injection (1 of 15 versus 5 of 14 patients) [135]. Injection of corticosteroids into the stricture (a method used for refractory peptic esophageal strictures) did not improve outcomes in a pilot randomized controlled trial [136].
Balloon dilation may be useful in situations in which it is desirable to postpone surgery. However, the significant risk of perforation, which substantially increases morbidity, must be considered.
Stenting — Placement of an expandable metal stent within colonic strictures has been described, but experience is limited, and the safety of this approach is uncertain [137].
Colorectal disease — Several alternatives are available for patients requiring elective surgery for colorectal Crohn's disease, ranging from temporary diverting ileostomy to resection of segments of diseased colon or even the entire colon and rectum. Although controversial, it appears that the conservative principles applied to disease involving the small intestine should also be applied to the surgical management of Crohn's colitis [138].
The optimal procedure depends in part upon the extent of the disease and the clinical setting:
Postoperative monitoring — Patients who have a retained rectum should undergo surveillance regularly after operation because of a small risk of cancer [147]. The optimal surveillance strategy remains controversial, although annual surveillance has been recommended. (See "Colorectal cancer surveillance in inflammatory bowel disease".)
Patients with severe Crohn's colitis requiring surgery are at increased risk of developing dysplasia and adenocarcinoma in the retained rectum [148]. In a retrospective review of 222 patients who required operative intervention for Crohn's colitis, there were five cases of dysplasia (2.3 percent) and six cases of adenocarcinoma (2.7 percent). In this small cohort, the risk factors for the development of dysplasia or adenocarcinoma included longer disease duration (over 17 years), extensive disease, and older age at diagnosis (38 years of age or older). These findings support colonoscopic screening and surveillance of patients with Crohn's colitis. (See "Colorectal cancer surveillance in inflammatory bowel disease".)
Recurrence — The postoperative recurrence rate for patients undergoing a resection and anastomosis is high. Endoscopic recurrence approaches 80 percent at one year, while the clinical recurrence rate is 10 to 15 percent per year [149-152]. However, in most series up to 20 percent of patients will not have a clinical recurrence even at 15 years after surgery [153]. Those with severe endoscopic or radiologic findings are at increased risk to have or develop symptoms (72 versus 42 percent in those with minimal disease in one series) [154]. An increased risk for reoperation has been associated with perforating disease and smoking [155].
A laparoscopic approach does not appear to decrease the risk of recurrence. A retrospective review of 89 patients undergoing laparoscopically resected primary ileocolonic Crohn’s colitis found recurrent disease in 61 percent [156]. The median time to recurrence was 13 months (range 1.3 months to 8.7 years). Only the presence of granulomas in the resected specimen was identified as a risk factor for time to recurrence, and these patients were almost three times more likely to develop a recurrence.
The recurrence rate is lower in patients with Crohn's colitis who undergo a total colectomy and ileostomy compared to those with disease involving other segments of the digestive tract. Such patients have only a 10 percent recurrence rate in the small intestine at 10 years [150]. A number of medical options are available that may reduce the risk of recurrence. (See "Medical prophylaxis of postoperative Crohn's disease".) A relatively aggressive approach should be considered in patients with diffuse and distal Crohn's colitis. Total proctocolectomy in properly selected patients is associated with low morbidity, a decreased risk of recurrence, and a longer time to recurrence [157].
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SUMMARY AND RECOMMENDATIONS — Surgical treatment is an important component of inflammatory bowel disease therapy since it can alleviate symptoms, address serious complications, improve quality of life, and, in some settings, be lifesaving. Surgery may be performed in both the emergent and elective setting.
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