Lymphoproliferative disorders with early lethality in mice deficient in Ctla-4

Science. 1995 Nov 10;270(5238):985-8. doi: 10.1126/science.270.5238.985.

Abstract

The role of the cell-surface molecule CTLA-4 in the regulation of T cell activation has been controversial. Here, lymph nodes and spleens of CTLA-4-deficient mice accumulated T cell blasts with up-regulated activation markers. These blast cells also infiltrated liver, heart, lung, and pancreas tissue, and amounts of serum immunoglobulin were elevated. The mice invariably became moribund by 3 to 4 weeks of age. Although CTLA-4-deficient T cells proliferated spontaneously and strongly when stimulated through the T cell receptor, they were sensitive to cell death induced by cross-linking of the Fas receptor and by gamma irradiation. Thus, CTLA-4 acts as a negative regulator of T cell activation and is vital for the control of lymphocyte homeostasis.

Publication types

  • Research Support, Non-U.S. Gov't
  • Comment

MeSH terms

  • Abatacept
  • Animals
  • Antigens, CD / analysis
  • Antigens, Differentiation / genetics
  • Antigens, Differentiation / physiology*
  • Apoptosis
  • B-Lymphocytes / immunology
  • CTLA-4 Antigen
  • Cells, Cultured
  • Concanavalin A / pharmacology
  • Female
  • Gamma Rays
  • Gene Targeting
  • Homeostasis
  • Immunoconjugates*
  • Immunoglobulins / blood
  • Immunophenotyping
  • Lymph Nodes / immunology
  • Lymph Nodes / pathology
  • Lymphocyte Activation*
  • Lymphoproliferative Disorders / immunology*
  • Lymphoproliferative Disorders / pathology
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Spleen / immunology
  • Spleen / pathology
  • T-Lymphocytes / immunology*
  • fas Receptor / metabolism

Substances

  • Antigens, CD
  • Antigens, Differentiation
  • CTLA-4 Antigen
  • Ctla4 protein, mouse
  • Immunoconjugates
  • Immunoglobulins
  • fas Receptor
  • Concanavalin A
  • Abatacept