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Primary cutaneous large B cell lymphoma, leg type

Authors
Eric Jacobsen, MD
Arnold S Freedman, MD
Rein Willemze, MD
Section Editors
Timothy M Kuzel, MD, FACP
John A Zic, MD
Deputy Editor
Alan G Rosmarin, MD

INTRODUCTION

Primary cutaneous B cell lymphoma (PCBCL) refers to those cases of B cell lymphoma that present in the skin when there is no evidence of extracutaneous disease at the time of diagnosis and after the completion of an initial staging evaluation. There are three main subtypes of PCBCL:

Primary cutaneous follicle center lymphoma (PCFCL)

Primary cutaneous large B cell lymphoma (PCLBCL), leg type

Primary cutaneous marginal zone lymphoma (PCMZL), included in the broader category of extranodal marginal zone B cell lymphoma

These appear to be unique entities with differing clinical presentation, pathologic features, prognosis, and treatment approach. This topic review will discuss primary cutaneous large B cell lymphoma; leg type.

                    

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Literature review current through: Nov 2016. | This topic last updated: Mon Oct 03 00:00:00 GMT+00:00 2016.
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