Practical aspects of nocturnal noninvasive ventilation in neuromuscular and chest wall disease
- Nicholas S Hill, MD
Nicholas S Hill, MD
- Professor of Medicine
- Tufts University School of Medicine
- Naomi R Kramer, MD
Naomi R Kramer, MD
- Assistant Professor of Medicine
- Warren Alpert Medical School of Brown University
- Section Editors
- Jeremy M Shefner, MD, PhD
Jeremy M Shefner, MD, PhD
- Section Editor — Neuromuscular Disease
- Professor and Chair of Neurology, Barrow Neurological Institute
- Professor of Neurology, University of Arizona, Phoenix
- Clinical Professor of Neurology, Creighton University
- Polly E Parsons, MD
Polly E Parsons, MD
- Editor-in-Chief — Pulmonary and Critical Care Medicine
- Section Editor — Critical Care
- Professor of Medicine
- University of Vermont College of Medicine
Noninvasive ventilation refers to mechanical ventilation without the need for an invasive interface (ie, an invasive artificial airway) between the ventilatory device and the patient. Noninvasive ventilation is now commonly used to assist ventilation in patients with a variety of chronic neuromuscular and chest wall diseases .
The incidence of respiratory muscle dysfunction varies among these different entities. In neuromuscular disease, the degree of compromise may differ significantly between respiratory and nonrespiratory muscles, and not all respiratory muscles may be similarly impaired. The clinical course also varies, as the rate of progression may differ enormously between individuals with the same disease (eg, amyotrophic lateral sclerosis) and respiratory muscle weakness may be:
●Completely reversible (Guillain-Barré syndrome)
●Reversible with treatment (myasthenia gravis)
●Relapsing (multiple sclerosis)
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