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Peeling skin syndrome

Authors
Eli Sprecher, MD, PhD
Liat Samuelov, MD
Section Editor
Jonathan A Dyer, MD
Deputy Editor
Rosamaria Corona, MD, DSc

INTRODUCTION

Peeling skin syndrome (PSS) is a heterogeneous group of rare autosomal recessive disorders characterized by superficial painless peeling and blistering of the skin without mucosal fragility [1,2]. The two major forms of PSS are acral PSS (APSS) and generalized PSS [3-6]. The latter is subclassified into noninflammatory or type A PSS and inflammatory or type B PSS [7,8].

This topic will review the pathogenesis, clinical features, and management of PSS. Congenital blistering diseases and keratinization disorders are discussed separately.

(See "Epidemiology, pathogenesis, classification, and clinical features of epidermolysis bullosa".)

(See "Diagnosis of epidermolysis bullosa".)

(See "Overview of the management of epidermolysis bullosa".)

                                       

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Literature review current through: Nov 2016. | This topic last updated: Tue Jun 16 00:00:00 GMT+00:00 2015.
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