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Management of coarctation of the aorta

Authors
Brojendra N Agarwala, MD
Emile Bacha, MD, FACS
Qi Ling Cao, MD
Ziyad M Hijazi, MD, MPH, FAAP, FACC, MSCAI, FAHA
Section Editors
David R Fulton, MD
Heidi M Connolly, MD, FASE
Deputy Editors
Carrie Armsby, MD, MPH
Susan B Yeon, MD, JD, FACC

INTRODUCTION

Coarctation of the aorta is a discrete narrowing of the thoracic aorta just distal to the left subclavian artery. The care of a patient with coarctation depends upon the severity of the coarctation, patient age, and clinical presentation.

The management of coarctation of the aorta including corrective treatment options and complications will be reviewed here. The clinical manifestations, natural history, and diagnosis of coarctation of the aorta are discussed separately. (See "Clinical manifestations and diagnosis of coarctation of the aorta".)

OVERVIEW

Management decisions for patients with coarctation of the aorta depend upon patient age, presentation, and the severity of the lesion.

Critical coarctation in infancy — Infants with severe ("critical") coarctation are at risk for developing heart failure and death when the ductus arteriosus closes. Identification of these patients is essential in order to maintain patency of the ductus prior to surgical repair. In addition, immediate treatment is required to stabilize patients with heart failure. (See "Clinical manifestations and diagnosis of coarctation of the aorta", section on 'Neonates' and "Identifying newborns with critical congenital heart disease", section on 'Clinical features'.)

Medical therapy consists of the following:

                                       

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Literature review current through: Nov 2016. | This topic last updated: Fri May 06 00:00:00 GMT+00:00 2016.
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