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Intestinal malrotation in children

Author
Mary L Brandt, MD
Section Editors
Jonathan I Singer, MD
Melvin B Heyman, MD, MPH
Deputy Editor
James F Wiley, II, MD, MPH

INTRODUCTION

An overview of the presentation, diagnosis, and treatment of intestinal malrotation in children will be presented here.

Intestinal malrotation in adults and congenital diaphragmatic hernia and abdominal wall defects are discussed separately. (See "Intestinal malrotation in adults" and "Omphalocele".)

EPIDEMIOLOGY

Rotational anomalies occur as a result of an arrest of normal rotation of the embryonic gut. Because rotational anomalies may remain asymptomatic throughout a person’s life span, the true incidence is not known. Nonrotation, a type of malrotation is an incidental finding on approximately 2 out of 1000 upper gastrointestinal contrast studies [1]. Symptomatic malrotation in neonates occurs with a frequency of about 1 in 6000 live births.

Traditionally, intestinal malrotation has been considered primarily a disease of infancy with infrequent occurrence beyond the first year of life [2,3]. However, analysis of 2744 cases of intestinal rotation in children up to 17 years of age obtained from a national hospital discharge database found the following [2]:

Presentation by one month of age: 30 percent

                       

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Literature review current through: Aug 2016. | This topic last updated: Sep 19, 2016.
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