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Interstitial lung disease in dermatomyositis and polymyositis: Clinical manifestations and diagnosis

Authors
Paul F Dellaripa, MD
Marc L Miller, MD
Section Editors
Ira N Targoff, MD
Kevin R Flaherty, MD, MS
Deputy Editors
Helen Hollingsworth, MD
Monica Ramirez Curtis, MD, MPH

INTRODUCTION

Dermatomyositis (DM) and polymyositis (PM) are classified as idiopathic inflammatory myopathies. Among patients with DM or PM, interstitial lung disease (ILD) is a major cause of morbidity and mortality. A general approach to the evaluation of ILD is provided separately. (See "Approach to the adult with interstitial lung disease: Clinical evaluation" and "Approach to the adult with interstitial lung disease: Diagnostic testing".)

In patients with DM or PM, ILD must be distinguished from other causes of pulmonary disease:

Infection

Drug-induced pneumonitis

Pneumomediastinum

                         

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Literature review current through: Nov 2016. | This topic last updated: Thu Dec 17 00:00:00 GMT+00:00 2015.
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