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Initial treatment of peripheral T cell lymphoma

Eric Jacobsen, MD
Arnold S Freedman, MD
Section Editor
Andrew Lister, MD, FRCP, FRCPath, FRCR
Deputy Editor
Alan G Rosmarin, MD


The peripheral T cell lymphomas (PTCL) are a heterogeneous group of generally aggressive neoplasms that constitute less than 15 percent of all non-Hodgkin lymphomas (NHLs) in adults. Among these, in decreasing frequency of occurrence, are:

Peripheral T cell lymphoma, not otherwise specified (PTCL, NOS)

Anaplastic large cell lymphoma, primary systemic type (ALCL)

Angioimmunoblastic T cell lymphoma (AITL)

Extranodal NK/T cell lymphoma, nasal type


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Literature review current through: Sep 2016. | This topic last updated: Mar 17, 2016.
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