Henoch-Schönlein purpura (immunoglobulin A vasculitis): Management
- Fatma Dedeoglu, MD
Fatma Dedeoglu, MD
- Assistant Professor of Pediatrics
- Harvard Medical School
- Susan Kim, MD, MMSc
Susan Kim, MD, MMSc
- Instructor of Pediatrics
- Children's Hospital, Boston
Henoch-Schönlein purpura (HSP), also called immunoglobulin A vasculitis (IgAV) , is the most common systemic vasculitis of childhood. Ninety percent of cases occur in the pediatric age group. In contrast to other forms of systemic vasculitis, HSP (IgAV) is usually self-limited and is characterized by a tetrad of clinical manifestations that vary in their presence and order of presentation:
●Palpable purpura in patients with neither thrombocytopenia nor coagulopathy
●Arthralgia and/or arthritis
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