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Henoch-Schönlein purpura (IgA vasculitis): Management

INTRODUCTION

Henoch-Schönlein purpura (HSP), also called IgA vasculitis (IgAV) [1], is the most common systemic vasculitis of childhood. Ninety percent of cases occur in the pediatric age group. In contrast to other forms of systemic vasculitis, HSP (IgAV) is usually self limited and is characterized by a tetrad of clinical manifestations that vary in their presence and order of presentation.

Palpable purpura in patients with neither thrombocytopenia nor coagulopathy

Arthralgia and/or arthritis

Abdominal pain

Renal disease

            

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Literature review current through: Aug 2014. | This topic last updated: Apr 8, 2013.
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References
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