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Head and neck sarcomas

Authors
Bruce E Brockstein, MD
Mihir K Bhayani, MD, FACS
Section Editors
Marshall R Posner, MD
David M Brizel, MD
Daniel G Deschler, MD, FACS
Russell S Berman, MD
Alberto S Pappo, MD
Deputy Editor
Diane MF Savarese, MD

INTRODUCTION

Head and neck sarcomas are rare tumors, and this makes rigorous study of clinical behavior difficult. As a result, treatment algorithms are drawn from retrospective case series and principles are derived from treatment of sarcomas at other sites, rather than from large clinical trials. Their study is also made more difficult by the diversity of histologic subtypes and the variable clinical behavior. Furthermore, the confining anatomy and proximity to vital structures makes even adherence to traditional margin-driven therapy challenging.

The demographics of head and neck sarcomas, the clinical behavior of the common subtypes, and general treatment principles will be reviewed here. An overview of the epidemiology, clinical presentation, histopathology, diagnostic evaluation, and staging of soft tissue and bone sarcomas, and a discussion of treatment for sarcomas arising at other sites are discussed elsewhere.

(See "Clinical presentation, histopathology, diagnostic evaluation, and staging of soft tissue sarcoma".)

(See "Osteosarcoma: Epidemiology, pathogenesis, clinical presentation, diagnosis, and histology".)

(See "Chondrosarcoma".)

                                       

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Literature review current through: Nov 2016. | This topic last updated: Tue Sep 06 00:00:00 GMT+00:00 2016.
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