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Ectopia lentis (dislocated lens) in children

Author
Kathryn M McCreery, FRCOphth, FRCSI, MRCPI
Section Editor
Evelyn A Paysse, MD
Deputy Editor
Carrie Armsby, MD, MPH

INTRODUCTION

Lens dislocation (ectopia lentis) in children may occur after trauma or in association with ocular or systemic disease. Dislocated lens in children will be discussed here. Cataracts and optical/visual rehabilitation of aphakic children are discussed separately. (See "Cataract in children".)

TERMINOLOGY

Subluxation is the term used when the lens is partially dislocated but remains attached to the ciliary body (figure 1) [1]. Luxation is the term used when the lens is completely detached from the ciliary body. Luxated lenses may be loose in the posterior chamber or can present in the anterior chamber.

EPIDEMIOLOGY

The prevalence of dislocated lenses is not known [1].

ETIOLOGY

Lens dislocation (ectopia lentis) in children may occur after trauma or in association with ocular or systemic disease. It is important to determine the etiology because the associated disorders have different requirements for monitoring and/or therapy.

Trauma — Dislocation of the lens (picture 1) may occur after blunt trauma to the head, orbit, or eye [1]. It occurs most commonly when the eye/orbit is hit directly with a high-energy projectile (eg, BB, golf ball, baseball).

        

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Literature review current through: Nov 2016. | This topic last updated: Tue Aug 11 00:00:00 GMT+00:00 2015.
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