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Cutis verticis gyrata

Author
Fiona Larsen, MBChB, FRACP
Section Editor
Jonathan A Dyer, MD
Deputy Editor
Rosamaria Corona, MD, DSc

INTRODUCTION

Cutis verticis gyrata (CVG) is a rare congenital or acquired scalp condition characterized by convoluted folds and deep furrows that resemble the surface of the cerebral cortex [1-3]. It may occur as a primary condition, often in association with neuropsychiatric or ophthalmologic abnormalities, or may be secondary to a number of localized or systemic inflammatory or neoplastic diseases. Cutis verticis gyrata has also been reported in association with several genetic syndromes, including Turner syndrome, Noonan syndrome, and craniosynostosis syndromes.

This topic will discuss the clinical presentation, diagnosis, and treatment of primary and secondary CVG. Other scalp disorders are discussed separately. (See "Approach to the patient with a scalp disorder".)

CLASSIFICATION

Cutis verticis gyrata is classified as primary, essential or nonessential, or secondary [3,4].

Primary essential cutis verticis gyrata occurs in isolation in otherwise normal individuals.

The primary nonessential form is associated with neuropsychiatric or ophthalmologic abnormalities.

          

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Literature review current through: Nov 2016. | This topic last updated: Mon Jun 13 00:00:00 GMT+00:00 2016.
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