Clinical manifestations, pathologic features, and diagnosis of extranodal NK/T cell lymphoma, nasal type
- Arnold S Freedman, MD
Arnold S Freedman, MD
- Section Editor — Lymphoproliferative Disorders
- Professor of Medicine
- Harvard Medical School
- Jon C Aster, MD
Jon C Aster, MD
- Professor of Pathology
- Harvard Medical School
The peripheral T cell lymphomas (PTCL) are a heterogeneous group of generally aggressive neoplasms that constitute less than 15 percent of all non-Hodgkin lymphomas (NHLs) in adults [1,2]. (See "Classification of the hematopoietic neoplasms".)
Among these, in decreasing frequency of occurrence, are:
●Peripheral T cell lymphoma, not otherwise specified (NOS)
●Anaplastic large cell lymphoma, primary systemic type
●Angioimmunoblastic T cell lymphomaTo continue reading this article, you must log in with your personal, hospital, or group practice subscription. For more information on subscription options, click below on the option that best describes you:
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- CLINICAL FEATURES
- PATHOLOGIC FEATURES
- Morphologic features
- - Growth pattern
- - Cell morphology
- Genetic features
- DIFFERENTIAL DIAGNOSIS
- NK cell leukemia
- Lymphomatoid granulomatosis
- EBV-positive mucocutaneous ulcer
- EBV-positive diffuse large B cell lymphoma, NOS
- Peripheral T cell lymphoma, unspecified
- Hepatosplenic T cell lymphoma
- Squamous cell carcinoma
- Nonkeratinizing nasopharyngeal carcinoma
- NK cell enteropathy