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Clinical manifestations, pathologic features, and diagnosis of angioimmunoblastic T cell lymphoma

Authors
Arnold S Freedman, MD
Jon C Aster, MD
Section Editor
Andrew Lister, MD, FRCP, FRCPath, FRCR
Deputy Editor
Alan G Rosmarin, MD

INTRODUCTION

The peripheral T cell lymphomas (PTCL) are a heterogeneous group of generally aggressive neoplasms that constitute less than 15 percent of all non-Hodgkin lymphomas (NHLs) in adults [1,2]. (See "Classification of the hematopoietic neoplasms".)

Among these, in decreasing frequency of occurrence, are:

Peripheral T cell lymphoma, not otherwise specified

Anaplastic large cell lymphoma, primary systemic type

Angioimmunoblastic T cell lymphoma

                 

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Literature review current through: Nov 2016. | This topic last updated: Tue Apr 05 00:00:00 GMT+00:00 2016.
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