Clinical manifestations and diagnosis of pulmonic stenosis in adults
- Karen Stout, MD
Karen Stout, MD
- Cardiology/Medicine and Pediatrics
- University of Washington
Stenosis of the pulmonary valve is a relatively common congenital defect, occurring in approximately 10 percent of children with congenital heart disease . There is a slight female predominance, and familial occurrence has been reported in 2 percent of cases .
Pulmonic stenosis in children is usually associated with a benign clinical course, and excellent treatment options are available for severe cases. Thus, there is a high rate of survival into adulthood. This topic will review the pathophysiology, clinical manifestations, and diagnosis of pulmonic stenosis. The natural history and treatment of this disorder are discussed separately. (See "Natural history and treatment of pulmonic stenosis in adults".)
Pulmonic stenosis can occur at three locations:
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- Valvular pulmonic stenosis
- - Associated conditions
- Subvalvular pulmonic stenosis
- Supravalvular pulmonic stenosis
- CLINICAL MANIFESTATIONS
- ADDITIONAL TESTS
- Cardiac catheterization
- Cardiac magnetic resonance imaging
- Infective endocarditis
- SUMMARY AND RECOMMENDATIONS